Decrease of urinary acid mucopolysaccharides in Hurler's syndrome after plasma infusion.
نویسندگان
چکیده
ORII, T., YAMAGUCHI, M., MINAMI, R. and NAKAO, T. Decrease of Urinary Acid Mueopolysaccharides in Hurler's Syndrome after Plasma Infusion. Tohoku J. exp. Med., 1974, 112 (4), 385-387 The fresh plasma infusion in patients affected by Hurler, Scheie or Morquio syndromes was followed by a decreased urinary excretion of chondroitin sulfate B or keratosulfate. Furthermore, in all of the patients the infusion was followed by an increased excretion of the non cetylpyridinium chloride precipitates. mucopolysaccharidosis; plasma infu sion
منابع مشابه
Diagnosis of Hurler's syndrome in the hospital laboratory and the determination of its genetic type.
The rare genetically determined disease now known as Hurler's syndrome, characterized by dwarfism, grotesque skeletal deformity, limitation of joint movement, deafness, hepatosplenomegaly, cardiac abnormality, characteristic facies, and perhaps clouding of the cornea and mental retardation (McKusick, 1960), was first described by Hunter (1917). For some years, the substance that accumulates in ...
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ورودعنوان ژورنال:
- The Tohoku journal of experimental medicine
دوره 112 4 شماره
صفحات -
تاریخ انتشار 1974